Mortality Risk Prediction in Scleroderma-Related Interstitial Lung Disease
نویسندگان
چکیده
منابع مشابه
Scleroderma-related interstitial lung disease
Scleroderma-related interstitial lung disease (SSc-ILD) is a pulmonary fibrosing disorder characterized by systemic inflammation and progressive scarring of the lungs that leads to respiratory failure. Although certain immunosuppressive therapies may slow disease progression, current treatment strategies are not curative; consequently, SSc-ILD continues to be a major cause of morbidity and mort...
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Introduction: Pulmonary involvement is the most common cause of mortality and disability in patients with systemic sclerosis and it significantly affects the quality of life in these patients. Therefore, early diagnosis and treatment of pulmonary involvement seems necessary in patients with SSc. In this study, we aimed to assess the health-related quality of life (HRQoL) in patients with Sclero...
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Pulmonary involvement is quite frequent in the development of progressive systemic sclerosis (PSS), a disease that affects the skin and internal organs and may present in various forms, especially as interstitial lung disease (ILD) or pulmonary hypertension (PH).(1) The incidence of pulmonary involvement varies depending on the population and on the methodology used for the diagnosis, reaching ...
متن کاملthe assessment of health-related quality of life in scleroderma-interstitial lung disease
introduction: pulmonary involvement is the most common cause of mortality and disability in patients with systemic sclerosis and it significantly affects the quality of life in these patients. therefore, early diagnosis and treatment of pulmonary involvement seems necessary in patients with ssc. in this study, we aimed to assess the health-related quality of life (hrqol) in patients with sclero...
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Interstitial lung disease is the most common complication and cause of death among patients with scleroderma. Scleroderma-related interstitial lung disease has usually been treated with cyclophosphamide; however, its effect was evaluated to be modest and long-term administration of this drug is associated with adverse effects. Herein, we report our clinical experience of administering pirfenido...
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ژورنال
عنوان ژورنال: Chest
سال: 2017
ISSN: 0012-3692
DOI: 10.1016/j.chest.2017.06.009